Last Updated: September 28, 2018
Hemangioblastomas are benign, World Health Organization (WHO) class I tumors that predominantly (>90%) occur within the posterior fossa. They constitute only 8% of adult posterior fossa tumors and only 1% of all intracranial tumors. These tumors typically originate near the fourth ventricle in the cerebellar hemispheres, vermis, or even the brainstem.
Up to 30% of the patients with hemangioblastomas suffer from Von Hippel Lindau (VHL) syndrome. Although rare, spinal hemangioblastomas can also occur, usually near the cervical or thoracic spinal cord. Most spinal hemangioblastomas are associated with a syrinx and can be easily overlooked in a patient who presents with posterior fossa symptoms.
Patients with a solitary hemangioblastoma lesion hav...